Glossary for Adult Congenital Heart Disease, K—K

Kartagener syndrome

Autosomal recessive syndrome consisting of situs inversus totalis, dextrocardia and defect of ciliary motility leading to sinusitis, bronchiectasis and sperm immobility. (Kartegener M. Zur Pathogenese der Bronchiektasien: Bronchiektasien bei Situs viscerum inversus. Beitr Klink Tuberkul 1933;28:231-234.)  (Kartagener M et al. Bronchiectasis with situs inversus. Arch Pediatr 1962;79:193-196.)  (Miller RD et al. Kartagener's syndrome. Chest 1972;62:130-136.)

Kommerell

See diverticulum of Kommerell.

Konno procedure (operation)

Repair of tunnel-like subvalvar LVOTO by aorto-ventriculoplasty. The operation involves enlargement of the LV outflow tract by inserting a patch in the ventricular septum, as well as aortic valve replacement and enlargement of the aortic annulus and ascending aorta. (Konno S, et al. A new method for prosthetic valve replacement in congenital aortic stenosis associated with hypoplasia of the aortic valve ring. J Thorac Cardiovasc Surg 1975;70:909-917.) In severe forms of LVOTO, a prosthetic-valve-containing conduit may be inserted between the left ventricular apex and descending aorta. (Didonato RM, et al. Left ventricular-aortic conduits in paediatric patients. J Thorac Cardiovasc Surg 1984;88:82-91.) (Frommelt PC, et al. Natural history of apical left ventricular to aortic conduits in paediatric patients. Circulation 1991;84 (suppl III):213-218.)