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• Cyanotic Defects
• Congenital Valve Defects

Aortic

Pulmonary

Tricuspid
• Coarctation of the Aorta
• Septal Defects
• Pregnancy and ACHD
 

Aortic Valve Defects (Stenosis and Insufficiency)


What are Aortic Valve Defects?
Blood from the heart’s left ventricle flows through the aortic valve into the aorta for distribution to the body. After each heartbeat, the aortic valve closes. This keeps blood from leaking back into the left ventricle. Normally the heart's aortic valve has three leaflets (tricuspid). Defective aortic valves usually have only two leaflets (bicuspid). This is called a bicuspid aortic valve.

Most bicuspid valves will function normally throughout life. In some cases, however, the valves deteriorate. They may become thick and narrowed (stenosis) or curled at the edges and leaky (insufficient).

Aortic stenosis is the most common valve disorder in the U.S. About one in 50 boys and 1 in 100 girls are born with the defect. Some of the defects are the result of a rare disorder called Marfan’s syndrome. Aortic valve disease is most common in men between the ages of 30 and 60.

Symptoms
Aortic valve stenosis and insufficiency may result in the following symptoms:

  • Shortness of breath
  • Chest pain during exercise
  • Dizziness or fainting
  • Arrhythmia
  • Reduced ability for physical activity.

If an aortic valve defect is suspected, an echocardiogram [link glossary\echocardiogram ] can help confirm the diagnosis. A chest X-ray may show calcium deposits in the narrowed aortic valve.

Additional tests may include:

Treatment Options
Mild to moderate valve disease may need no treatment. It also may be managed with medications that may slow or halt degeneration of the valve and relieve symptoms. In some cases, however, the valve will need to be surgically repaired or replaced.

Surgical Treatment - If stenosis severely restricts blood flow from the heart, pressure builds up in the heart’s left ventricle. The heart has to work harder. When this occurs, the valve must be widened through catheterization or surgically replaced.

  • Balloon valvotomy catheterization. In this procedure, a thin flexible tube (catheter) is inserted through an artery in the groin or arm and threaded into the heart. Once the tube reaches the aortic valve, a balloon device on the end of the catheter is inflated. This stretches the narrowed valve leaflets and permits blood to flow more freely.
  • If the aortic valve has become severely insufficient, it will probably need to be replaced. There are several ways to surgically replace the valve:
    • The Ross procedure. In this procedure, the aortic valve is removed and replaced by the pulmonary valve. The pulmonary valve is then replaced with a donor pulmonary valve.
    • Aortic valve replacement with a donor valve.
    • Aortic valve replacement with a mechanical valve.

Ongoing Care
Routine follow-up is important for adults with aortic valve disease. Valve status can change as patients age, regardless of whether they have had catheterization or valve replacement. All patients with congenital aortic valve defects are at risk for bacterial endocarditis, an infection of the heart’s valves or inner lining (endocardium). Before having certain dental or surgical procedures performed, it may be necessary to take preventive antibiotics.

 

Need an appointment? Request one online 24 hours a day, 7 days a week; or call 800-789-PENN (7366) to speak to a referral counselor.

 
 

 

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