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• Cyanotic Defects
• Congenital Valve Defects

Aortic

Pulmonary

Tricuspid
• Coarctation of the Aorta
• Septal Defects
• Pregnancy and ACHD
 

Congenital Valve Defects


What Are Congenital Valve Defects?
Heart valves regulate the flow of blood through the heart's four chambers — the two upper "holding" chambers called the atria and the two lower "pumping" chambers called ventricles.

Each ventricle has a one-way inlet valve and a one-way outlet valve. In the right ventricle, the inlet valve is the tricuspid valve and the outlet valve is the pulmonary valve. In the left ventricle, the inlet valve is the mitral valve and the outlet valve is the aortic valve. Each valve consists of leaflets (flaps) that open and close in one direction.

Symptoms may include:

  • Shortness of breath when physically active or lying down
  • Dizziness or fainting
  • A feeling of pressure in the chest
  • A sensation of a rapid or irregular heartbeat (palpitations)
  • Weakness
  • Anxiety attacks (mitral valve defect)
  • Swelling (edema) in the feet, ankles or abdomen (pulmonary valve defect)
  • Several pound weight gain within a day or so (pulmonary valve defect)

A heart murmur — a "swishing" sound of blood flow heart by a stethoscope — may be noticed. If suspected, valve defects may be diagnosed with the following tests:

Defects of the heart valves are grouped according to which valve is involved:

  • Aortic valve defects
  • Mitral valve defects
  • Pulmonary valve defects
  • Tricuspid valve defects

Treatment Options
Treatment of heart valve disease depends on the valve and the severity of symptoms. If valve disease is mild to moderate, no treatment may be necessary. In some cases, medications may be prescribed to alleviate symptoms.

Severely narrowed (stenotic) or leaking (regurgitating) valves require surgery by experienced cardiologists. Penn Cardiac Care surgeons perform many valve replacements and repairs every year. Patients who have had this procedure do well.

The following procedures are available to repair and replace diseased valves:

  • Annuloplasty - This surgical technique is performed on the valve's annulus — the ring of tissue that supports the valve’s leaflets — to make it smaller.
  • Cardiac catheterization - This procedure uses a balloon-tipped catheter to widen the valve as the balloon is inflated.
  • Structural repair - Surgical techniques to repair the structure will replace or shorten the valve’s supportive cords — the chordae tendineae and papillary muscles.
  • Valvuloplasty - This surgical technique involves surgically separating, pleating or cutting out a part of a valve leaflet.
  • Valve replacement - This surgical technique involves removing the defective valve and replacing it with a biological or mechanical valve. Most valve replacements are of the mitral or aortic valves.

Follow-up Care
Patients with valve disease should be monitored at regular medical checkups by experienced cardiologists. Patients with congenital valve disease are at risk for bacterial endocarditis, an infection of the heart’s valves or inner lining (endocardium.) Before having certain dental or surgical procedures performed, it may be necessary to take preventive antibiotics.

 

Need an appointment? Request one online 24 hours a day, 7 days a week; or call 800-789-PENN (7366) to speak to a referral counselor.

 
 

 

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