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• Cyanotic Defects
• Congenital Valve Defects

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• Coarctation of the Aorta
• Septal Defects
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Pulmonary Valve Stenosis


What Is Pulmonary Valve Stenosis?
The pulmonary valve allows blood to flow from the heart’s lower right "pumping" ventricle into the pulmonary artery. The pulmonary artery carries deoxygenated blood to the lungs to be reoxygenated. Normally, the pulmonary valve has three leaflets (flaps). If the leaflets are not properly developed, the valve may become narrow (stenosis) or leaky (insufficient). Stenosis or insufficiency can range from moderate to severe.

Pulmonary valve stenosis accounts for about 10 percent of congenital heart defects.

Symptoms of pulmonary stenosis include:

  • Shortness of breath
  • Fatigue
  • Fainting
  • Chest pain
  • Bluish color to skin (cyanosis)

A heart murmur may be heard by stethoscope when there is stenosis. The following tests may be used to confirm the diagnosis:

Treatment Options
If the narrowing is severe, the pulmonary valve must be opened to increase blood flow to the lungs. This may be done by cardiac catheterization [link glossary/cardiac catheterization], in which a balloon is expanded to enlarge the opening. If the insufficiency is severe, an operation is required to repair or replace the pulmonary valve.

Ongoing Care
If pulmonary stenosis or insufficiency is severe, ongoing care by an experienced cardiologist is necessary to check for re-stenosis or increased insufficiency, irregular heat beat (arrhythmias) and signs of strain or dilation of the right ventricle. Some patients with residual defects, such as a leaky valve (regurgitation), may benefit from medications to lower blood pressure and help the heart pump better. Patients with pulmonary valve stenosis are at risk for bacterial endocarditis, an infection of the heart’s valves or inner lining (endocardium.) Before having certain dental or surgical procedures performed, it may be necessary to take preventive antibiotics.

 

Need an appointment? Request one online 24 hours a day, 7 days a week; or call 800-789-PENN (7366) to speak to a referral counselor.

 
 

 

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